The cutaneous manifestations of the Klippel‐Trenaunay‐Weber syndrome
Identifieur interne : 00E740 ( Main/Exploration ); précédent : 00E739; suivant : 00E741The cutaneous manifestations of the Klippel‐Trenaunay‐Weber syndrome
Auteurs : D. Viljoen [Afrique du Sud] ; N. Saxe [Afrique du Sud] ; J. Pearnj [Australie] ; P. BeightonSource :
- Clinical and Experimental Dermatology [ 0307-6938 ] ; 1987-01.
Abstract
The Klippel‐Trenaunay‐Weber syndrome (KTWS) is the widely accepted eponym for the condition of angioosteohypertrophy. The clinical features of limb overgrowth and various vascular malformations have been previously well‐described, but the spectrum of dermatological manifestations of the KTWS is less well‐documented. For this reason we have evaluated the natural history of the cutaneous lesions in 20 affected individuals. It has emerged that the hitherto unreported problem of aseptic cellulilis is a frequent and potentially severe complication in the KTWS.
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DOI: 10.1111/j.1365-2230.1987.tb01845.x
Affiliations:
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Pearnj</name><affiliation wicri:level="1"><country xml:lang="fr">Australie</country><wicri:regionArea>University of Queensland Royal Children's Hospital, Brisbane</wicri:regionArea><wicri:noRegion>Brisbane</wicri:noRegion></affiliation></author><author><name sortKey="Beighton, P" sort="Beighton, P" uniqKey="Beighton P" first="P." last="Beighton">P. Beighton</name><affiliation><wicri:noCountry code="no comma">M. R. C. Unit for Inherited Disorders of the Skeleton</wicri:noCountry></affiliation></author></analytic><monogr></monogr><series><title level="j" type="main">Clinical and Experimental Dermatology</title><title level="j" type="alt">CLINICAL EXPERIMENTAL DERMATOLOGY</title><idno type="ISSN">0307-6938</idno><idno type="eISSN">1365-2230</idno><imprint><biblScope unit="vol">12</biblScope><biblScope unit="issue">1</biblScope><biblScope unit="page" from="12">12</biblScope><biblScope unit="page" to="17">17</biblScope><biblScope unit="page-count">6</biblScope><publisher>Blackwell Publishing Ltd</publisher><pubPlace>Oxford, UK</pubPlace><date type="published" when="1987-01">1987-01</date></imprint><idno type="ISSN">0307-6938</idno></series></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0307-6938</idno></seriesStmt></fileDesc><profileDesc><textClass></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">The Klippel‐Trenaunay‐Weber syndrome (KTWS) is the widely accepted eponym for the condition of angioosteohypertrophy. The clinical features of limb overgrowth and various vascular malformations have been previously well‐described, but the spectrum of dermatological manifestations of the KTWS is less well‐documented. For this reason we have evaluated the natural history of the cutaneous lesions in 20 affected individuals. It has emerged that the hitherto unreported problem of aseptic cellulilis is a frequent and potentially severe complication in the KTWS.</div></front></TEI><affiliations><list><country><li>Afrique du Sud</li><li>Australie</li></country></list><tree><noCountry><name sortKey="Beighton, P" sort="Beighton, P" uniqKey="Beighton P" first="P." last="Beighton">P. Beighton</name></noCountry><country name="Afrique du Sud"><noRegion><name sortKey="Viljoen, D" sort="Viljoen, D" uniqKey="Viljoen D" first="D." last="Viljoen">D. Viljoen</name></noRegion><name sortKey="Saxe, N" sort="Saxe, N" uniqKey="Saxe N" first="N." last="Saxe">N. Saxe</name></country><country name="Australie"><noRegion><name sortKey="Pearnj, J" sort="Pearnj, J" uniqKey="Pearnj J" first="J." last="Pearnj">J. Pearnj</name></noRegion></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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